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. 1983 Jul;112(1):27–36.

The pathology of the feline model of mucopolysaccharidosis I.

M E Haskins, G D Aguirre, P F Jezyk, R J Desnick, D F Patterson
PMCID: PMC1916323  PMID: 6407329

Abstract

Five cats with feline alpha-L-iduronidase-deficient mucopolysaccharidosis were studied. Membrane-bound cytoplasmic inclusions were present in central nervous system neurons, hepatocytes, chondrocytes, vascular and splenic smooth muscle cells, bone marrow leukocytes, and fibroblasts of the skin, eye, and cardiac valves. The lesions in these cats closely resemble those described in human patients with mucopolysaccharidosis I H (Hurler syndrome).

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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