Table 1 Prognosis of amyotrophic lateral sclerosis with respiratory onset.
| Mean survival time from | Mean (months) | SD | |
|---|---|---|---|
| Symptom onset to death | 30.6 | 20.1 | |
| Symptom onset to death or PAV | 27 | 14.9 | |
| Diagnosis to death | 13.4 | 16.7 | |
| Diagnosis to death or PAV | 9.8 | 9.7 | |
| Symptom onset to death (NIPPV offered and tolerated) | 36.4 | 16 | |
| Symptom onset to death (no NIPPV) | 21.5 | 16 | |
| Onset to death/PAV if initial FVC was <50% (n = 6) | 29.5 | 14.1 | |
| Onset to death/PAV if initial FVC was >50% (n = 15) | 26 | 15.6 |
FVC, forced vital capacity; NIPPV, non‐invasive positive pressure ventilation; PAV, permanent assisted ventilation.