Table 1. Gene Set Analysis demonstrates a signature of DNA damage in FRDA patients.
Set Name | Score | p-Value | FDR |
BLEO_HUMAN_LYMPH_HIGH_4HRS_UP | −0.37 | 0.044 | 0.6916 |
GENOTOXINS_ALL_24HRS_REG | −0.4663 | 0.044 | 0.6916 |
MMS_HUMAN_LYMPH_LOW_4HRS_DN | −1.1264 | 0.01 | 0.5726 |
MMS_MOUSE_LYMPH_HIGH_4HRS_UP | −0.7369 | 0.002 | 0.4453 |
P53GENES_ALL | 0.3779 | 0.04 | 0.9698 |
UVB_NHEK1_C6 | −0.4047 | 0.022 | 0.6203 |
UVB_NHEK1_DN | −0.4473 | 0.014 | 0.5726 |
UVB_NHEK2_DN | −0.3615 | 0.012 | 0.5726 |
UVB_NHEK3_C2 | −0.7741 | 0.004 | 0.5726 |
UVC_HIGH_ALL_DN | −0.4171 | 0.006 | 0.5726 |
UVC_HIGH_D1_DN | −0.4286 | 0.032 | 0.668 |
UVC_HIGH_D2_DN | −0.366 | 0.064 | 0.7433 |
UVC_HIGH_D7_DN | −0.4576 | 0.018 | 0.5726 |
UVC_HIGH_D9_DN | −0.733 | 0.008 | 0.5726 |
UVC_TTD_4HR_DN | −0.5704 | 0.006 | 0.5726 |
UVC_TTD_8HR_DN | −0.3107 | 0.044 | 0.6916 |
UVC_TTD_ALL_DN | −0.4737 | 0.008 | 0.5726 |
UVC_TTD-XPCS_COMMON_DN | −0.4533 | 0.012 | 0.5726 |
UVC_XPCS_4HR_DN | −0.5225 | 0.014 | 0.5726 |
UVC_XPCS_4HR_UP | −0.6511 | 0.028 | 0.645 |
UVC_XPCS_8HR_DN | −0.5428 | 0.008 | 0.5726 |
UVC_XPCS_ALL_DN | −0.5414 | 0.006 | 0.5726 |
UV-CMV_UNIQUE_HCMV_6HRS_DN | −0.2488 | 0.02 | 0.5938 |
GSA was performed using the Molecular Signatures Database. Significantly enriched gene sets included 23 sets associated to genotoxic stress response.